Lhermitte-Duclos disease associated with Cowden's disease--case report.
نویسندگان
چکیده
A 49-year-old Japanese male with Lhermitte-Duclos disease subsequently developed a very rare association with Cowden's disease. Partial tumor removal established the diagnosis of Lhermitte-Duclos disease. Follow-up examinations discovered the presence of Cowden's disease. Long-term follow-up of patients with Lhermitte-Duclos disease is essential to identify signs of Cowden's disease, which carries the risk of developing malignancy.
منابع مشابه
Recurrent Lhermitte-Duclos disease: report of two cases and association with Cowden's disease.
Two cases of Lhermitte-Duclos disease (LDD), one associated with Cowden's disease, are reported. Both demonstrated recurrence long after initial surgical resection. There is a propensity for occurrence in the left cerebellar hemisphere. On MR there is hypointensity on T1-weighted images and moderately high signal on T2-weighted images, with parallel linear striations on the surface of the lesio...
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ورودعنوان ژورنال:
- International journal of oral and maxillofacial surgery
دوره 24 5 شماره
صفحات -
تاریخ انتشار 1995